Web弯刀综合征(Scimitar syndrome)是罕见的先天性心脏病，发病率1/50 000 [] ，特征为部分性或完全性单侧肺静脉异位引流入下腔静脉，以右肺多见，常常伴有同侧的肺发育不良以及来自体循环的侧支血管供应发育不良的肺叶。 因异位引流入下腔静脉的右肺静脉X线胸片表现类似弯曲的土耳其弯刀影，故称为 ... WebBackground: Thirty-two patients with scimitar syndrome were seen in the period between 1975 and 1995. There were 11 male and 21 female patients. Median age at diagnosis was 7 months (mean 7.7 years, range 1 day to 70 years). Patients in whom the diagnosis was made during the first year of life (infantile group, n = 19) had more severe symptoms and …
The Complete Reference for Scimitar Syndrome - 1st Edition
Scimitar syndrome, or congenital pulmonary venolobar syndrome, is a rare congenital heart defect characterized by anomalous venous return from the right lung (to the systemic venous drainage, rather than directly to the left atrium). This anomalous pulmonary venous return can be either partial (PAPVR) or total … See more The anomalous venous return forms a curved shadow on chest x-ray such that it resembles a scimitar. This is called the Scimitar Sign. Associated abnormalities include right lung hypoplasia with associated … See more Surgical correction should be considered in the presence of significant left to right shunting (Qp:Qs ≥ 2:1) and pulmonary hypertension. This involves creation of an inter-atrial baffle to redirect the pulmonary venous return into the left atrium. Alternatively, the … See more • Holt, PD; Berdon, WE; Marans, Z; Griffiths, S; Hsu, D (February 2004). "Scimitar vein draining to the left atrium and a historical review of the … See more The diagnosis is made by transthoracic or transesophageal echocardiography and selective pulmonary angiography. More recently by CT … See more Scimitar syndrome was first described by George Cooper and Raoul Chassinat in 1836 regarding a rare syndrome that has an abnormal pulmonary vein that drains into See more Web31 Jan 2004 · The scimitar syndrome is a congenital anomalous connection of the pulmonary vein with the inferior vena cava. On the chest radiograph, the vein produces a vascular shadow to the right of the heart that descends toward the diaphragm, resembling a scimitar, which is a short curved Turkish sword. liberty barrows
Scimitar Syndrome: Anyone else have this? » Mayo Clinic Connect
WebScimitar Syndrome Interrupted Inferior Vena Cava Tricuspid Valve Abnormalities Ebstein Anomaly Tricuspid Atresia Right Ventricular and Pulmonary Outflow Abnormalities … Web11 Apr 2024 · Katy’s story. Hi, I am Katy and I am 25 years old. I work as Deputy Manager at a mental health Crisis Centre and live in Oxford. When I was 10 weeks old, I was diagnosed with Scimitar syndrome, a rare congenital heart defect which affects approximately one in 100,000 people. Web19 Dec 2024 · Scimitar syndrome is a type of rare congenital heart defect. Babies born with this condition may be asymptomatic, or have severe symptoms which require surgical … mcgrath gosford real estate